November 12, 2014
Notes: Chen, Zhiyao
Research Support, Non-U.S. Gov’t
Exp Biol Med (Maywood). 2013 Jun;238(6):687-95. doi: 10.1177/1535370213490629.
Author Address: Affiliated Union Hospital, Fujian Medical University, Fujian, 350001, China.
Reference Type: Journal Article
Record Number: 5016Author: Chun, S. W., Choi, J. S., Kang, B. D., Kim, Y. J., Han, K. J., Cho, H. G., Oh, H. E. and Cho, J. H.
Title: [A case of IgG4 associated sclerosing cholangitis without clinical manifestations of autoimmune pancreatitis]
Journal: Korean J Gastroenterol
Short Title: [A case of IgG4 associated sclerosing cholangitis without clinical manifestations of autoimmune pancreatitis]
Alternate Journal: The Korean journal of gastroenterology = Taehan Sohwagi Hakhoe chi
ISSN: 1598-9992 (Print)
Accession Number: 23954964
Anti-Inflammatory Agents/therapeutic use
Bile Ducts, Intrahepatic/pathology/ultrasonography
Cholangiopancreatography, Endoscopic Retrograde
Cholangitis, Sclerosing/complications/*diagnosis/drug therapy
Common Bile Duct/pathology/ultrasonography
Tomography, X-Ray Computed
Abstract: IgG4-related systemic diseases are characterized by a diffuse or mass forming inflammatory reaction rich in lymphocytes and IgG4-positive plasma cells (lymphoplasmacytic infiltration), fibrosclerosis of variable organs and obliterative phlebitis. They usually involve various organs including the pancreas, bile duct, gallbladder, salivary gland, retroperitoneum, kidney, lung, and prostate. However, most of them are accompanied by autoimmune pancreatitis, and good response to steroid treatment is one of the hallmarks of this disease. We report a case of an 67-year-old man with IgG4 associated sclerosing cholangitis, who was diagnosed by endoscopic retrograde cholangiopancreatography and successfully treated with steroid therapy.